The liver is an important organ in the body which has a wide range of functions including detoxification, protein synthesis and production of biochemicals necessary for digestion. Excess glucose is stored in the liver in the form of glycogen but when the body cannot break down, then it results into glycogen storage disease which results in increased glucose accumulation in the liver. The significant effects of glucose accumulation is swelling of the liver as well as the kidneys. Glycogen is a form of sugar which is stored in the liver and muscles. It is broken down into glucose to give energy when needed. Glycogen Storage Disease is also known as Von Gierke Disease.

WHAT ARE THE CAUSES OF GLYCOGEN STORAGE DISEASE?

This condition occurs when the body lacks the enzyme that releases glucose from glycogen which causes abnormal amounts of glycogen to build up in certain tissues. When glycogen is not broken down properly, it leads to low blood sugar. The cause of this disease is also inherited. If both parents carry a non-working copy of the gene related to this condition, each of their children has a 25% chance of developing the disease.

WHAT ARE THE SYMPTOMS OF GLYCOGEN STORAGE DISEASE?

Easy bruising and nosebleeds.
Constant hunger and need to eat often
Fatigue
Irritability
Puffy cheeks
Thin chest and limbs
Swollen belly

DIAGNOSIS

Tests That Include Are:-

Biopsy of liver or kidney
Genetic testing
Lactic acid blood test
Blood sugar test
Triglyceride level
Uric acid blood test

If a patient suffering from this disease, test results will show low blood sugar and high levels of lactate which are produced from lactic acid and blood fats and uric acid.

Physician will also form a physical exam. The exam may show signs of -

Delayed puberty
Enlarged liver
Gout
Liver tumors
Stunted growth or failure to grow
Inflammatory bowel disease

TREATMENT

The goal of the treatment for glycogen storage disease is to avoid low blood sugar. A medicine to lower uric acid in the blood and decrease the risk for gout may be prescribed.

Analysis of glycogen storage disease with an Ayurvedic view point, it is understood to be an outcome of a toxic accumulation of morbid metabolic toxins in the body. This is due to the diminished execution of the digestive and metabolic activities of the body- both at the level of GIT as well as at the tissue level. As the Ayurvedic principles in such clinical conditions lay down, the treatment is aimed at ensuring a proper mobilisation of the accumulated morbid metabolic toxins at the tissue level and to enhance the digestive and metabolic ability of the organs involved in GIT. Simultaneously, with the clearing off the accumulated toxins, the rejuvenation of the individual cells of the body is also given equal importance.

Keeping these Ayurvedic principles in consideration, Planet Ayurveda has designed a pack especially for the treatment of glycogen storage disease which corrects the diarrhoea and abdominal distension, corrects the functions of the liver and the kidney.

GLYCOGEN STORAGE DISEASE PACK OF PLANET AYURVEDA CONSISTS OF

Navkarshik Churna
Fenugreek Capsules
Punarnava Mandoor Tablets
Liver detox Capsules
Ashwagandha Capsules
Echinacea Capsules

Herbal Remedies for Glycogen Storage Disease

1. Navkarshik Churna

Navkarshik Churan of Planet Ayurveda works on the root cause of the problem by correcting purine metabolism, correcting liver metabolism, cleanses the blood, breaks uric acid crystals and clear them away. Navkarshik Churna is one of the best herbal remedy for gout thus a boon for glycogen storage disease patients because it cleanses the toxins accumulated in the system.

Dosage: 1 teaspoonful twice daily with plain water after meals.

2. Fenugreek Capsules

Fenugreek Capsules of Planet Ayurveda have numerous health benefits. Fenugreek is known for maintaining healthy blood glucose level thus helps in maintaining healthy glucose level in the patients suffering from glycogen storage disease.

Dosage: 1 capsules twice daily after half an hour of meal with plain water.

3. Punarnava Mandoor Tablets

Punarnava Mandoor Tablets of Planet Ayurveda are classical ayurvedic tablets for many health conditions. They are excellent to remove toxins from the blood, helps in decreasing urea/creatinine and other toxins from the body. They are also quite beneficial in renal failure, liver failure, fluid accumulation, fatty liver and many other problems. Thus, intake of Punarnava Mandoor Tablets by the patient of glycogen storage disease is quite beneficial as it removes the morbid toxins.

Dosage: 2 tablets twice a day with plain water after meals.

4. Liver Detox Capsules

Liver Detox Capsules of Planet Ayurveda helps to keep the liver healthy by removing the accumulated toxins in the liver thus quite beneficial for the patients of glycogen storage disease as it is the condition in which liver is unable to store the glycogen. These capsules are also beneficial in the conditions like – fatty liver, elevated liver enzymes- SGOT, SGPT, liver cirrhosis etc.

Dosage: 1 capsule twice a day with plain water.

5. Ashwagandha Capsules

Ashwagandha (Withania somnifera) capsules of Planet Ayurveda are useful in various debilitating conditions, neuropathy, fatigue, loss of weight. It enhances stamina both physical as well as mental. It can be given to growing children as well as to old age people.

Dosage: 1 capsule twice daily with plain water after meals.

6. Echinacea Capsules

Echinacea is also known as "King of Bitters". It has been widely used to treat different kinds of infections. It is widely used in many Ayurvedic formulations also known as "Kalmegh" which means dark cloud. Echinacea of Planet Ayurveda is an herbal supplement which possesses immune-stimulant, anti-parasitic, anti-biotic and anti-parasitic properties. It is used in the treatment of hepatitis, flatulence, gastric disorders, bowel complaints etc. This product of Planet Ayurveda is quite beneficial for all the liver disorders thus acting as a boon for the patients of glycogen storage disease.